What is Lennox-Gastaut syndrome?

What is Lennox-Gastaut syndrome?

Lennox-Gastaut syndrome (LGS) is a type of epilepsy. Patients with LGS experience many different types of seizures including: Tonic – stiffening of the body. Atonic – temporary loss of muscle tone and consciousness, causing the patient to fall. Atypical absence – staring episodes.

What is the life expectancy for Lennox-Gastaut syndrome?

Longitudinal studies have found that a minority of patients with LGS eventually could work normally, but 47-76% still had typical characteristics (mental retardation, treatment-resistant seizures) many years after onset and required significant help (eg, home care, institutionalization).

Is Lennox-Gastaut syndrome fatal?

The progressive intellectual impairment associated with Lennox-Gastaut syndrome means that many patients require full-time care throughout life. The short-term mortality of Lennox-Gastaut syndrome is approximately 4-7%. This is largely due to seizure-related fatal accidents.

What is Dravet Syndrome?

Definition. Dravet syndrome, previously called severe myoclonic epilepsy of infancy (SMEI), is an epilepsy syndrome that begins in infancy or early childhood and can include a spectrum of symptoms ranging from mild to severe.

Can Lennox-Gastaut syndrome go away?

Lennox-Gastaut syndrome (LGS) is a severe form of childhood epilepsy with multiple types of seizures. In 1 out of 4 people, no cause can be found. About 2 to 5% of children with epilepsy have LGS. Usually, LGS persists through childhood and adolescence to adult years.

What is the rarest type of epilepsy?

Dravet Syndrome

• Dravet syndrome is a rare, drug-resistant epilepsy that begins in the first year of life in an otherwise healthy infant.
• Most cases are due to severe SCN1A gene mutations.
• Most children develop varying degrees of developmental disability.

Can Lennox-Gastaut syndrome be cured?

There is no cure for the disorder. Complete recovery, including freedom from seizures and normal development, is very rare. The prognosis for individuals with Lennox-Gastaut syndrome varies. There is no cure for the disorder.

What is the rarest form of epilepsy?

Dravet syndrome is a rare, catastrophic, lifelong form of epilepsy that begins in the first year of life with frequent and/or prolonged seizures. Previously known as Severe Myoclonic Epilepsy of Infancy (SMEI) 80% of people have a mutation in their SCN1A gene.

How long do kids with Dravet live?

Dravet syndrome is a rare, severe, and lifelong form of epilepsy (seizure disorder). Most people affected by this condition have a good life expectancy. The disease typically starts in the first year of life, and around 80-85% of the children survive into adulthood.

What’s the worst type of epilepsy?

Several different types of seizures can be seen in Dravet syndrome, the most dangerous of which are tonic-clonic seizures, sometimes called a generalized seizure or a grand-mal seizure.